Pulmonary Valvular Stenosis with Intact Ventricular Septum and Right Aortic Arch.

Pulmonary valvular stenosis with right-sided aortic arch and an intact ventricular septum is a rare anomaly. Brock and Campbell (1950) and Abrahams and Wood (1951) stated that the aortic arch was left-sided in simple pulmonary valvular stenosis. Three years later, Campbell (1954) reported one patient with a right aortic arch from a series of 75 cases of pulmonary valvular stenosis with an intact ventricular septum: details of this patient's history and the methods of exclusion of a ventricular septal defect were not specified. A search has failed to reveal any other reported cases of pulmonary stenosis and right aortic arch without an associated ventricular septal defect. This paper reports a second instance of this particular combination of defects.